منابع مشابه
Recalcitrant hypocalcaemia in autoimmune enteropathy.
Autoimmune polyendocrinopathy candidiasis ectodermal dystrophy syndrome is a monogenic disorder associated with autoimmune destruction of both endocrine and nonendocrine tissues. The classic triad includes candidiasis, hypoparathyroidism, and Addison disease. Up to 25% of patients with autoimmune polyendocrinopathy candidiasis ectodermal dystrophy syndrome also have gastrointestinal manifestati...
متن کاملThe Spectrum of Autoimmune Enteropathy
Chronic, unexplained diarrhea in children younger than 3 months old was first characterized as “intractable diarrhea” [1]. The term “protracted diarrhea” was used later to describe infants with frequent and loose stools severe enough to often require parenteral alimentation as nutritional support [2]. The differential diagnosis of enteropathies in infancy and childhood includes inherited epithe...
متن کاملSystemic vasculitis complicating infantile autoimmune enteropathy.
An infant with unexplained sideroblastic anaemia and severe protracted diarrhoea due to autoimmune gut disease is reported. Despite treatment with an exclusion diet and immunosuppressive agents she developed a severe systemic vasculitic illness. Intensive treatment with plasmapheresis resulted in resolution of the vasculitic process but the child subsequently died after overwhelming septicaemia.
متن کاملSeronegative Adult Autoimmune Enteropathy in a Male Traveler
Autoimmune enteropathy (AIE) is rare but damaging. The lack of consistent objective findings makes diagnosis a challenge. A 45-year-old male developed noninfectious diarrhea with significant weight loss and electrolyte abnormalities. Computed tomography delineated enteritis. Colonoscopy and esophagogastroduodenoscopy showed villous atrophy, chronic inflammation, and ulceration of the terminal i...
متن کاملFrom autoimmune enteropathy to the IPEX (immune dysfunction, polyendocrinopathy, enteropathy, X-linked) syndrome.
The term autoimmune enteropathy (AIE) was applied to a form of "intractable diarrhoea" with serum gut autoantibodies, characterized by male predominance, early onset, poor response to parenteral nutrition and several autoimmune diseases, mainly type 1 diabetes. In recent years the vague concept of AIE has became more precise thanks to the discovery of its genetic and molecular basis. The FOXP3 ...
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ژورنال
عنوان ژورنال: Advances in Digestive Medicine
سال: 2020
ISSN: 2351-9797,2351-9800
DOI: 10.1002/aid2.13234